MAR 15, 2016
Management of Corneal Perforation in Ehlers-Danlos Syndrome
By Ali A AlRajhi, MD
AAO 2015
Cornea/External Disease
Ehlers Danlos Syndrome (EDS) presents with thin cornea and sclera. One patient who sustained trauma in both eyes later developed corneal perforation that could not be managed by amniotic membrane (AM) and fibrin glue application. A fashionable corneal transplantation fixed on the area of perforation with fibrin glue and AM application was successful in sealing the perforation with 3 years of follow-up. Lens aspiration of this case was associated with perforation of thin sclera — then managed with sclera patch graft. This video illustrates methods of managing this other cases in which the cornea is susceptible to perforation/laceration and present challenges in management.