A 13-month-old child presented with iris heterochromia, buphthalmos and spontaneous hyphema. On further examination, a temporal cystic ciliary body lesion associated with rubeosis iridis was found adjacent to the lens. A clinical diagnosis of medulloepithelioma was made, and the eye was enucleated because of concern for malignancy, the presence of anterior segment neovascularization and discomfort. Medulloepithelioma was confirmed by pathology exam.

Sarwat Salim, MD, Yale Eye Center, New Haven, Conn. and David S. Walton, MD, Massachusetts Eye and Ear Infirmary, Boston.