By Jose N. Vargas Galveia, MD; Ana C. Rodrigues Almeida, MD; Maria Rodrigues; Marta E. Guedes, MD; Tiago B. Ferreira, MD; Ana Maria Bivar, MD; Alberto Cardosa, MD
    Cataract/Anterior Segment

    Anterior lenticonus is a conic accentuation of the anterior convexity of the lens. It is a key finding in Alport syndrome (25% incidence). In this video we will review the pathophysiology of Alport syndrome and present its ocular and systemic manifestations. Regarding treatment, we will place a special emphasis on the specificities of cataract surgery, particularly on capsulorrhexis' construction. As an example we will present the case of a patient with bilateral anterior lenticonus and cataract. His best spectacle corrected visual acuity (BSCVA) preoperatively was 0,4 OD and 0,3 OS. He was submitted to facoemulsification with placement of Acrisof® toric lens (SN60T6) in the capsular bag. Postoperatively the uncorrected visual acuity (UCVA) was 1,0 OU.