A 7-year-old boy presented with a limbal dermoid about 6.5-mm in diameter at the inferior esclerocorneal limbus of his left eye. Best-corrected visual acuity was 20/20 in his right eye and 12/20 in his left. Manifest refraction was +2.00/–0.75 × 175 degrees in his right and +2.00/–4.00 × 145 degrees in his left. The authors used a trephine of 6.5-mm encompassing the whole lesion. The lesion was dissected with scalpel and scissors until the clear cornea was reached. The donor button was obtained with a 6.5-mm trephine, laid over the area of the dermoid, and the cornea edge fixed with a 10-0 nylon suture. Lamellar keratoplasty to treat limbal dermoids at childhood is described as the best therapeutic option, and excellent visual results can be achieved in the majority of the authors' patients.