Port-wine stain (PWS; also known as port-wine nevus or nevus flammeus) is a congenital vascular malformation that manifests as a flat red or pink cutaneous lesion. It may lighten during the first year of life but then tends to become darker, thicker, and more nodular over time. PWS is associated with Sturge-Weber and Klippel-Trénaunay-Weber syndromes (see Chapter 28) and is seen in combination with ocular melanosis in phakomatosis pigmentovascularis. Glaucoma can occur in affected eyes (see Chapter 22). Lasers can be used to lighten the affected areas.
Excerpted from BCSC 2020-2021 series: Section 10 - Glaucoma. For more information and to purchase the entire series, please visit https://www.aao.org/bcsc.