In the autosomal recessive disorder ectopia lentis et pupillae, the lens and the pupil are displaced in opposite directions. The pupil is irregular, usually slit shaped, and displaced from the normal position. The dislocated lens may bisect the pupil or may be completely luxated from the pupillary space. This disorder is usually bilateral but not symmetric. Characteristically, the iris dilates poorly. Associated ocular anomalies include severe axial myopia, retinal detachment, enlarged corneal diameter, cataract, and abnormal iris transillumination.