A medulloepithelioma (diktyoma) originates from the nonpigmented epithelium of the ciliary body and most often presents as an iris mass during the first decade of life. Secondary glaucoma, hyphema, and ectopia lentis et pupillae or sectoral cataract (Fig 21-21) are less frequent initial manifestations. This rare lesion shows a spectrum of clinical and pathologic characteristics, ranging from benign to malignant. Although distant metastasis is rare, local invasion can lead to death. Teratoid elements are often present. Enucleation is usually required and is curative in most cases.
Figure 21-21 Sectoral cataract adjacent to medulloepithelioma.
(Courtesy of Ken K. Nischal, MD.)
Excerpted from BCSC 2020-2021 series: Section 10 - Glaucoma. For more information and to purchase the entire series, please visit https://www.aao.org/bcsc.