MAR 10, 2020
5th Annual Global Video Contest
Pediatric Ophth/Strabismus, Retina/Vitreous, Trauma
We present a case of an 8-year-old child with Ehlers-Danlos Syndrome and a chronic inferior retinal detachment that was repaired with vitrectomy. The patient had a history of prior surgery in that eye related to trauma at the age of 3 and was aphakic. There was severe nasal scleromalacia likely related to his underlying connective tissue disorder and the prior trauma/surgery. A 23-G vitrectomy setup was initiated. There was continuous leakage around the nasal cannula and it failed to remain in position. The sclerotomy then enlarged significantly and caused transient hypotony with additional complications, including choroidal effusions, hyphema, and a large subretinal hemorrhage, that were managed.