2020–2021 BCSC Basic and Clinical Science Course™
6 Pediatric Ophthalmology and Strabismus
Part II: Pediatric Ophthalmology
Chapter 21: Disorders of the Anterior Segment
Abnormalities of Peripheral Corneal Transparency
Cornea Plana
Cornea plana is a pathognomonic phenotype of flat cornea, indistinct limbus, shallow anterior chamber, hyperopia, and associated accommodative esotropia (Fig 21-4); it is specific for biallelic KERA mutations. Refractive correction and monitoring for glaucoma, which may develop later in life, are the mainstays of treatment.
Excerpted from BCSC 2020-2021 series: Section 10 - Glaucoma. For more information and to purchase the entire series, please visit https://www.aao.org/bcsc.