Usher Syndrome Symptoms
The main visual symptom of Usher syndrome is loss of vision from retinitis pigmentosa (RP).
In people with RP, the light-sensing cells in the retina slowly degenerate (die). These cells are called rods and cones. This causes a gradual loss of vision. With most forms of RP, rods start dying first. This causes a loss of side and night vision. When the cones begin dying, the result is loss of color perception and central (reading) vision. Generally, after many years, blindness results.