• Courtesy of André Salgado Araújo Marques, MD, Fernanda Vaz
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    Retina/Vitreous

    Idiopathic Macular Telangiectasia Type 2 or Perifoveal Telangiectasia. It is an uncommon disorder characterized by telangiectatic vessels in the juxtafoveolar region of one or both eyes. Also commonly a bilateral disease, it can be asymmetric and may appear as a unilateral process early in the disease. Patients often present with complaints of blurred vision, metamorphopsia, or paracentral scotomas. The image is of a fluorescein angiography (FA) and optical coherence tomography (OCT) of a middle-aged woman presenting with progressive bilateral visual acuity decrease. The FA shows early exudation of the outer capillary network, mostly temporally and mainly in the right eye, followed by diffuse late staining. OCT demonstrates small foveal cystoid cavities in both eyes. Both oral carbonic anhydrase inhibitors and intravitreal anti-VEGF treatments were tried, but unfortunately with poor results.