Cataract Surgery in Spherophakia

Spherophakia is a rare congenital disorder characterized by anomalous changes in the shape and dimensions of the eye's lens. The presence of poorly developed and abnormally weak zonules leads to a reduction in lens diameter, a more spherical shape, and an increase in anteroposterior thickness. This condition may present as an isolated disorder or be associated with other familial conditions. Although many patients with spherophakia are asymptomatic, severe cases may display changes in refractive error, such as high myopia, and increased susceptibility to lens subluxation, cataracts, and glaucoma. The surgical management of spherophakia involves the extraction of the abnormal spherical lens and the implantation of an artificial intraocular lens. In this video, Dr. Matthias Gerl presents a case of a 21-year-old patient with bilateral spherophakia who underwent cataract surgery with 3-piece IOL implantation, focusing on the challenges that require particular attention from surgeons and the techniques used to overcome them.

Financial Disclosures: Dr. Matthias Gerl discloses no financial relationships.